ICD-10 Code D57.811 – Other sickle-cell disorders with acute chest syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D57.811 – Other sickle-cell disorders with acute chest syndrome
What it is
This code identifies acute chest syndrome occurring in a sickle-cell disorder that is not otherwise classified elsewhere. It signals a serious pulmonary complication associated with sickling and requires documentation of both the underlying disorder and the acute chest syndrome.
Clinical signs
Common findings include chest pain, fever, cough, shortness of breath, or new pulmonary infiltrates on imaging. Clinical features vary; refer to documentation.
When to use this code
Use this code when the record documents acute chest syndrome in a patient with an “other” sickle-cell disorder. You should see clear linkage between the sickle-cell condition and the chest syndrome in the provider’s note. If the type of sickle-cell disorder is specified more precisely, code that documented type instead.
Do not use for
Do not assign this code for uncomplicated sickle-cell disease without acute chest syndrome. Do not use it when the chart does not document acute chest syndrome or when a more specific sickle-cell diagnosis is clearly stated.
Coding tip
Check that the provider documents both the sickle-cell disorder and the acute chest syndrome before assigning D57.811.