ICD-10 Code D57.02 – Hb-SS disease with splenic sequestration (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D57.02 – Hb-SS disease with splenic sequestration
What it is
This code identifies sickle cell anemia with an episode of splenic sequestration, where sickled red blood cells become trapped in the spleen. It applies to patients with Hb-SS disease and an acute splenic enlargement event.
Clinical signs
Typical findings include sudden splenic enlargement, abdominal pain, and signs of acute anemia or hypovolemia. Clinical features vary; refer to documentation.
When to use this code
Use D57.02 when the provider documents Hb-SS disease and specifically states splenic sequestration. This is appropriate for an acute sequestration episode in a patient with sickle cell anemia. If the record only notes splenomegaly or sickle cell disease without sequestration, check documentation.
Do not use for
Do not use this code for other sickle cell crises, uncomplicated Hb-SS disease, or splenic enlargement without sequestration. Check documentation if the chart does not clearly link the spleen event to Hb-SS disease.
Coding tip
Code the condition only when the provider documents splenic sequestration, not just abdominal pain or anemia.