ICD-10 Code L10.81 – Paraneoplastic pemphigus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L10.81 – Paraneoplastic pemphigus
What it is
Paraneoplastic pemphigus is an autoimmune blistering disorder linked to an underlying malignancy. It causes painful mucosal and skin involvement and is coded when the diagnosis is documented.
Clinical signs
Typical findings include severe oral erosions, mucosal blistering, and polymorphous skin lesions. Clinical features vary; refer to documentation.
When to use this code
Use L10.81 when the record specifically documents paraneoplastic pemphigus, including suspected or confirmed cases tied to a neoplasm. You may code it from specialist notes, discharge summaries, or pathology reports if the diagnosis is stated clearly.
Do not use for
Do not use this code for other pemphigus types, such as pemphigus vulgaris or foliaceus, unless paraneoplastic pemphigus is documented. Check documentation when the note only says blistering disease or autoimmune bullous disorder.
Coding tip
Verify the exact pemphigus subtype in the chart before assigning L10.81.