ICD-10 Code L10.0 – Pemphigus vulgaris (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L10.0 – Pemphigus vulgaris
What it is
L10.0 identifies pemphigus vulgaris, an autoimmune blistering disorder that affects the skin and mucous membranes. It reflects a diagnosis of this specific pemphigus subtype, not a general blistering rash.
Clinical signs
Typical findings include fragile blisters, painful erosions, and mucosal involvement, especially in the mouth. Clinical features vary; refer to documentation for the exact distribution and severity.
When to use this code
Use L10.0 when the provider documents pemphigus vulgaris by name or clearly describes this diagnosis. It is appropriate for confirmed cases with skin, oral, or other mucosal lesions consistent with the disorder.
Do not assign it for unspecified pemphigus or for other blistering diseases unless the record explicitly supports pemphigus vulgaris. Check documentation when the note only says “pemphigus” or “autoimmune blistering disease.”
Do not use for
Do not use this code for bullous pemphigoid, dermatitis herpetiformis, or other non-pemphigus blistering conditions. If the record lacks a specific diagnosis, use the more accurate documented term.
Coding tip
Confirm that the provider names pemphigus vulgaris specifically; vague documentation should not be assumed to mean L10.0.