ICD-10 Code L10.3 – Brazilian pemphigus [fogo selvagem] (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L10.3 – Brazilian pemphigus [fogo selvagem]
What it is
L10.3 identifies Brazilian pemphigus, also called fogo selvagem, a rare autoimmune blistering skin disorder. It is a form of pemphigus that primarily affects the skin and is documented by this specific diagnosis.
Clinical signs
Typical findings include fragile blisters, erosions, and crusted lesions on the skin. Clinical features vary; refer to documentation if the chart does not clearly identify pemphigus with the Brazilian form.
When to use this code
Use L10.3 when the provider documents Brazilian pemphigus or fogo selvagem as the diagnosis. It is appropriate when the record supports this named pemphigus subtype rather than a broader pemphigus category. If the note is nonspecific, check documentation before coding.
Do not use for
Do not use this code for other pemphigus types, such as unspecified pemphigus or mucosal-predominant disease, unless the chart specifically states Brazilian pemphigus. Do not assume the diagnosis from blistering alone.
Coding tip
Code L10.3 only when the provider names fogo selvagem or Brazilian pemphigus explicitly in the assessment.