ICD-10 Code L10.1 – Pemphigus vegetans (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L10.1 – Pemphigus vegetans
What it is
L10.1 identifies pemphigus vegetans, a rare autoimmune blistering disorder and a variant of pemphigus vulgaris. It causes chronic skin and mucosal lesions that can become thickened, wart-like, or vegetative.
Clinical signs
Typical findings include erosions, flaccid blisters, and moist, vegetating plaques, often in skin folds or around the mouth. Clinical features vary; refer to documentation.
When to use this code
Use L10.1 when the provider documents pemphigus vegetans by name or clearly describes this specific pemphigus variant. You may also use it when pathology or specialist notes confirm the diagnosis. If the record only says pemphigus without subtype, check documentation.
Do not use for
Do not use this code for other pemphigus forms, such as pemphigus vulgaris or foliaceus, unless pemphigus vegetans is specifically documented. Do not assume it from nonspecific blistering or dermatitis.
Coding tip
Code the exact pemphigus subtype stated in the chart; if the subtype is unclear, query the provider before assigning L10.1.