ICD-10 Code E76.29 – Other mucopolysaccharidoses (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.29 – Other mucopolysaccharidoses
What it is
E76.29 identifies mucopolysaccharidosis types that do not fit a more specific ICD-10-CM code. Use it for a documented inherited lysosomal storage disorder involving abnormal glycosaminoglycan breakdown.
Clinical signs
Clinical features vary; refer to documentation. Common findings in mucopolysaccharidoses may include coarse facial features, skeletal abnormalities, developmental delay, organ enlargement, or corneal clouding.
When to use this code
Use this code when the provider documents “other mucopolysaccharidosis,” an unspecified subtype, or a named type not separately indexed in ICD-10-CM. It also applies when the record confirms mucopolysaccharidosis but does not identify a more specific category. Check documentation for the exact type before coding.
Do not use for
Do not use E76.29 when the record supports a specific mucopolysaccharidosis code, such as a named subtype with its own entry. Do not assign it for unrelated storage disorders or for suspected disease without confirmation.
Coding tip
Look for the exact subtype in the assessment, genetics note, or problem list before defaulting to E76.29.