ICD-10 Code E76.3 – Mucopolysaccharidosis, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.3 – Mucopolysaccharidosis, unspecified
What it is
This code identifies mucopolysaccharidosis when the subtype is not specified in the record. It refers to a lysosomal storage disorder with impaired breakdown of glycosaminoglycans.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include coarse facial features, skeletal abnormalities, organ enlargement, developmental delay, or progressive functional decline.
When to use this code
Use E76.3 when the provider documents mucopolysaccharidosis but does not name a specific type. Apply it for confirmed diagnoses, problem lists, or discharge summaries that remain nonspecific. If the record identifies a specific MPS subtype, code that instead.
Do not use for
Do not use this code when the chart clearly names a specific mucopolysaccharidosis type. Check documentation if the condition is only suspected, ruled out, or described with a different storage disorder.
Coding tip
Query the provider when the subtype is missing, because a more specific mucopolysaccharidosis code may be available.