ICD-10 Code E76.211 – Morquio B mucopolysaccharidoses (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.211 – Morquio B mucopolysaccharidoses
What it is
E76.211 identifies Morquio B mucopolysaccharidosis, a rare inherited lysosomal storage disorder. It is used when documentation specifies the Morquio B subtype rather than another mucopolysaccharidosis.
Clinical signs
Clinical features vary; refer to documentation. Typical references describe skeletal dysplasia, short stature, and joint abnormalities, with possible corneal and cardiac involvement depending on the case.
When to use this code
Use this code when the provider documents Morquio B mucopolysaccharidosis, MPS IVB, or an equivalent diagnosis. Code it from confirmed problem lists, specialist notes, or discharge summaries when the subtype is clearly identified.
If the record only says mucopolysaccharidosis or Morquio syndrome without specifying B, check documentation before coding. You should not assume the subtype from genetic testing alone unless the diagnosis is explicitly stated.
Do not use for
Do not use this code for Morquio A mucopolysaccharidosis or other mucopolysaccharidosis types. Do not assign it when the chart is nonspecific or the diagnosis is only suspected.
Coding tip
Verify the exact MPS subtype in the provider’s final diagnosis before assigning E76.211.