ICD-10 Code E34.50 – Androgen Insensitivity Syndrome, Unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E34.50 – Androgen insensitivity syndrome, unspecified
What it is
E34.50 identifies androgen insensitivity syndrome when the record does not specify a complete or partial form. It refers to a genetic condition in which the body has reduced or absent response to androgens.
Clinical signs
Clinical features vary; refer to documentation. Commonly noted findings may include atypical sexual development, undervirilized genitalia, or primary amenorrhea, depending on the type and age at presentation.
When to use this code
Use this code when the provider documents androgen insensitivity syndrome but does not specify the subtype. It also fits cases where the record confirms the diagnosis without further detail. If the note identifies complete or partial androgen insensitivity, code the documented specificity instead.
Do not use for
Do not use E34.50 for other disorders of sex development or for ambiguous genitalia without a documented diagnosis of androgen insensitivity syndrome. Check documentation if the subtype is stated elsewhere in the record.
Coding tip
Assign the unspecified code only when the chart lacks a clearer AIS subtype.