ICD-10 Code E34.5 – Androgen insensitivity syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E34.5 – Androgen insensitivity syndrome
What it is
Androgen insensitivity syndrome is a condition in which the body cannot respond normally to androgens. It can lead to atypical sexual development despite a typical 46,XY karyotype.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include absent or incomplete male genital development, female-appearing external genitalia, or undescended testes.
When to use this code
Use E34.5 when the provider documents androgen insensitivity syndrome, including complete or partial forms if not coded elsewhere more specifically. You may also use it when the diagnosis is confirmed in the record and the note describes abnormal androgen response or sex development findings.
Do not use for
Do not use this code for other disorders of sexual development unless androgen insensitivity is specifically documented. Check documentation if the record only mentions ambiguous genitalia, hypogonadism, or chromosomal findings without this diagnosis.
Coding tip
Code only when the clinician clearly states androgen insensitivity syndrome; otherwise, query for clarification.