ICD-10 Code E71.3 – Disorders of fatty-acid metabolism (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.3 – Disorders of fatty-acid metabolism
What it is
E71.3 identifies inherited or acquired disorders that affect the body’s ability to break down fatty acids for energy. These conditions can cause energy shortage, especially during fasting, illness, or exercise.
Clinical signs
Clinical features vary; refer to documentation. Commonly reported findings include hypoglycemia, weakness, lethargy, vomiting, or episodes triggered by fasting or stress. Some patients have cardiomyopathy, liver involvement, or muscle symptoms.
When to use this code
Use E71.3 when the record documents a fatty-acid oxidation or metabolism disorder without a more specific code. Apply it for confirmed congenital metabolic disease, or when the provider clearly diagnoses a fatty-acid metabolism defect.
Choose the more specific code if the chart names a defined subtype. If the diagnosis is only suspected, documented as a family history, or not confirmed, check documentation before coding.
Do not use for
Do not use this code for general lipid disorders, obesity, or nutritional problems. Also avoid it when the record names a different metabolic condition or when the diagnosis is unconfirmed.
Coding tip
Look for the exact disorder name in the assessment and code the most specific confirmed diagnosis available.