ICD-10 Code E71.128 – Other disorders of propionate metabolism (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.128 – Other disorders of propionate metabolism
What it is
E71.128 identifies inherited disorders that affect propionate metabolism, a pathway the body uses to break down certain nutrients. Use it when documentation specifies another propionate metabolism disorder not classified elsewhere.
Clinical signs
Clinical features vary; refer to documentation. Reported findings may include metabolic decompensation, poor feeding, vomiting, lethargy, or developmental concerns in affected patients.
When to use this code
Use this code when the provider documents a specific propionate metabolism disorder that does not fit a more exact ICD-10-CM code. It is appropriate for confirmed diagnoses, not for screening or family history alone. Check documentation if the metabolic disorder is named but not further specified.
Do not use for
Do not use this code for unspecified metabolic disorders or for conditions with a more precise ICD-10-CM diagnosis. Do not assign it when documentation only mentions evaluation for a metabolic problem.
Coding tip
Code the most specific documented metabolic disorder first, and query the provider if the record only says “propionate disorder” or is unclear.