ICD-10 Code E71.30 – Disorder of fatty-acid metabolism, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.30 – Disorder of fatty-acid metabolism, unspecified
What it is
This code identifies a disorder affecting the body’s ability to break down fatty acids for energy. Use it when the record confirms a fatty-acid metabolism disorder but does not name a more specific type.
Clinical signs
Clinical features vary; refer to documentation. Commonly documented findings may include episodes of hypoglycemia, lethargy, vomiting, or metabolic decompensation, but you should code only what is clearly stated.
When to use this code
Use E71.30 when the provider documents a fatty-acid oxidation or metabolism disorder and the specific subtype is not identified. It is appropriate for confirmed congenital or inherited metabolic disease when the chart remains nonspecific. If the record names a particular fatty-acid disorder, choose that more specific code instead.
Do not use for
Do not use this code for general malnutrition, nonspecific hypoglycemia, or an unspecified metabolic disorder without fatty-acid involvement. Check documentation if the diagnosis is only suspected.
Coding tip
Query for the exact fatty-acid disorder name before defaulting to E71.30.