ICD-10 Code L10.4 – Pemphigus erythematosus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L10.4 – Pemphigus erythematosus
What it is
L10.4 identifies pemphigus erythematosus, a rare autoimmune blistering disorder that combines features of pemphigus and lupus-like skin involvement. It is used when the diagnosis is specifically documented.
Clinical signs
Typical findings include superficial blisters, erosions, crusting, and scaly red plaques, often on sun-exposed skin. Clinical features vary; refer to documentation.
When to use this code
Use L10.4 when the clinician documents pemphigus erythematosus by name, including overlap presentations with cutaneous lupus features. It may also apply when the record clearly supports this specific subtype rather than another pemphigus form. Check documentation if the note is nonspecific.
Do not use for
Do not use this code for unspecified pemphigus, pemphigus vulgaris, or lupus without documented pemphigus erythematosus. If the chart does not clearly state this diagnosis, code the documented condition instead.
Coding tip
Confirm the exact diagnosis wording in the assessment, because L10.4 is specific and should not be assigned from vague blistering or rash descriptions alone.