ICD-10 Code J84.841 – Neuroendocrine cell hyperplasia of infancy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code J84.841 – Neuroendocrine cell hyperplasia of infancy
What it is
J84.841 identifies neuroendocrine cell hyperplasia of infancy, a rare infant lung disorder involving excessive pulmonary neuroendocrine cells. It is used when documentation names this specific diagnosis.
Clinical signs
Clinical features vary; refer to documentation. Typical references describe persistent tachypnea, hypoxemia, and respiratory distress in infancy, with findings that support diffuse small-airway or interstitial lung disease.
When to use this code
Use this code when the provider documents neuroendocrine cell hyperplasia of infancy, often after evaluation for unexplained chronic respiratory symptoms in an infant. Code it from the confirmed diagnosis, not from nonspecific breathing complaints alone. Check documentation if the chart uses older or uncertain terminology.
Do not use for
Do not use this code for general neonatal respiratory distress, transient tachypnea, or other interstitial lung diseases unless NEC is specifically documented. Check documentation when the diagnosis is only suspected.
Coding tip
Assign J84.841 only when the record clearly states this exact condition or an accepted synonym.