ICD-10 Code J84.1 – Other Interstitial Pulmonary Diseases with Fibrosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code J84.1 – Other interstitial pulmonary diseases with fibrosis
What it is
J84.1 identifies fibrotic interstitial lung disease not classified elsewhere. It is used when documentation describes interstitial pulmonary fibrosis or a similar fibrosing process affecting the lung interstitium.
Clinical signs
Common findings include progressive shortness of breath, dry cough, and imaging evidence of interstitial fibrosis. Clinical features vary; refer to documentation.
When to use this code
Use J84.1 when the provider documents other interstitial pulmonary disease with fibrosis, pulmonary fibrosis, or fibrotic interstitial lung disease and no more specific code applies. It is appropriate when the record supports chronic fibrotic lung involvement rather than an acute infection or edema. Check documentation if the exact interstitial lung disease subtype is named.
Do not use for
Do not use this code for idiopathic pulmonary fibrosis or other interstitial lung diseases with a more specific ICD-10-CM code. Do not assign it when fibrosis is not documented.
Coding tip
Code the most specific interstitial lung disease term documented, and use J84.1 only when fibrosis is clearly stated but no better code is available.