ICD-10 Code H47.039 – Optic nerve hypoplasia, unspecified eye (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H47.039 – Optic nerve hypoplasia, unspecified eye
What it is
Use this code for congenital underdevelopment of the optic nerve when the affected eye is not specified. The optic nerve is smaller than normal, which can limit visual signal transmission.
Clinical signs
Findings may include reduced visual acuity, nystagmus, strabismus, or an abnormal optic disc on eye examination. Clinical features vary; refer to documentation.
When to use this code
Use H47.039 when the provider documents optic nerve hypoplasia and does not identify the right or left eye. It is appropriate for congenital cases confirmed by ophthalmic examination or imaging. If laterality is stated, code the specified eye instead.
Do not use for
Do not use this code for acquired optic atrophy, optic neuritis, or other optic nerve disorders. If the record specifies a different eye or a more specific diagnosis, code that instead.
Coding tip
Check the note for laterality; unspecified-eye codes should be used only when the documentation truly lacks that detail.