ICD-10 Code H47.033 – Optic nerve hypoplasia, bilateral (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H47.033 – Optic nerve hypoplasia, bilateral
What it is
Optic nerve hypoplasia is an underdevelopment of the optic nerves present from birth. Bilateral means both optic nerves are affected, which can reduce visual input to the brain.
Clinical signs
Findings may include reduced visual acuity, nystagmus, strabismus, and small optic discs on eye exam. Clinical features vary; refer to documentation.
When to use this code
Use H47.033 when the provider documents bilateral optic nerve hypoplasia as the confirmed diagnosis. It also fits ophthalmology or neurology notes describing congenital optic nerve underdevelopment in both eyes. Check documentation if the record only says “optic nerve abnormality” or “vision loss” without this specific diagnosis.
Do not use for
Do not use this code for unilateral optic nerve hypoplasia, which has a different code. Do not assign it when the chart mentions suspected disease only or another optic nerve disorder. Check documentation.
Coding tip
Confirm laterality in the assessment, not just the exam findings, before assigning H47.033.