ICD-10 Code G71.0349 – Limb girdle muscular dystrophy due to other sarcoglycan dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.0349 – Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
What it is
This code identifies a limb-girdle muscular dystrophy caused by dysfunction in sarcoglycan proteins other than the more specific listed types. Use it for a hereditary muscle disorder affecting the shoulder and pelvic girdles.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty rising from a chair, climbing stairs, or lifting the arms. Clinical features vary; refer to documentation for the specific sarcoglycan subtype and confirmed diagnosis.
When to use this code
Use this code when the record states limb-girdle muscular dystrophy due to other sarcoglycan dysfunction and does not name a more specific sarcoglycan defect. It is appropriate for confirmed genetic or specialist diagnoses documented in the chart. If the subtype is unclear, check documentation before coding.
Do not use for
Do not use it for nonspecific muscle weakness, other muscular dystrophies, or limb-girdle muscular dystrophy with a different identified cause. Check documentation if the provider has not specified sarcoglycan involvement.
Coding tip
Code only when the provider documents this exact etiology; otherwise, query for clarification or use the most specific confirmed diagnosis.