ICD-10 Code G71.035 – Limb girdle muscular dystrophy due to anoctamin-5 dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.035 – Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
What it is
This code identifies limb girdle muscular dystrophy caused by anoctamin-5 dysfunction, a hereditary muscle disorder. It is used when documentation specifies ANO5-related disease affecting the shoulder and hip girdle muscles.
Clinical signs
Typical findings include slowly progressive weakness of proximal muscles, especially in the hips and shoulders. Clinical features vary; refer to documentation for the specific pattern, family history, and any genetic confirmation.
When to use this code
Use this code when the provider documents limb girdle muscular dystrophy due to ANO5 mutation, anoctamin-5 dysfunction, or an equivalent genetic diagnosis. It may also apply when the record clearly links the muscular dystrophy to ANO5 testing or specialist assessment. Check documentation if the cause is not explicit.
Do not use for
Do not use this code for unspecified limb girdle muscular dystrophy or other muscular dystrophy types without ANO5 involvement. Do not assign it when the record only notes muscle weakness or myopathy without a confirmed diagnosis.
Coding tip
Code G71.035 only when the documentation names ANO5-related limb girdle muscular dystrophy; otherwise, query for specificity.