ICD-10 Code G71.0342 – Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.0342 – Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
What it is
This code identifies a specific limb-girdle muscular dystrophy caused by beta sarcoglycan dysfunction. It is a hereditary muscle disease that mainly affects the shoulder and pelvic girdles.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty climbing stairs, rising from a chair, or lifting the arms. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents limb-girdle muscular dystrophy with beta sarcoglycan dysfunction, or an equivalent confirmed diagnosis. You should also use it when genetic or specialist documentation clearly identifies this subtype. Check documentation if the record only says muscular dystrophy without the specific cause.
Do not use for
Do not use this code for unspecified muscular dystrophy, other limb-girdle subtypes, or weakness without a confirmed dystrophy diagnosis. If the subtype is not documented, code the condition that is actually stated.
Coding tip
Match the code to the exact genetic or clinical subtype documented, not just the general limb-girdle muscular dystrophy label.