ICD-10 Code G71.0341 – Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.0341 – Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
What it is
This code identifies limb-girdle muscular dystrophy caused by alpha sarcoglycan dysfunction. It refers to a hereditary muscle disorder that mainly weakens the muscles around the hips and shoulders.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty rising from a chair, climbing stairs, or lifting the arms. Clinical features vary; refer to documentation.
When to use this code
Use this code when the record specifically documents limb-girdle muscular dystrophy due to alpha sarcoglycan dysfunction, including confirmed genetic or specialist diagnosis. You may also use it when the clinician clearly links the dystrophy to alpha sarcoglycan involvement. Check documentation if the subtype is not stated.
Do not use for
Do not use this code for other limb-girdle muscular dystrophy subtypes or for unspecified muscular dystrophy. If the chart only says “muscular dystrophy” or “myopathy,” you need more specific documentation.
Coding tip
Code the documented subtype exactly; if alpha sarcoglycan dysfunction is not named, do not assume this code.