ICD-10 Code G40.833 – Dravet syndrome, intractable, with status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.833 – Dravet syndrome, intractable, with status epilepticus
What it is
This code identifies Dravet syndrome, a severe epileptic encephalopathy, when seizures remain intractable and the patient is in status epilepticus. Use it for documented Dravet syndrome with ongoing difficult-to-control seizures.
Clinical signs
Clinical features vary; refer to documentation. Typical records note recurrent seizures beginning in early childhood, developmental concerns, and prolonged or repeated seizure activity consistent with status epilepticus.
When to use this code
Use this code when the provider documents Dravet syndrome and clearly states that seizures are intractable. It also requires documentation of status epilepticus, not just a history of prolonged seizures. If the note does not specify both elements, check documentation before coding.
Do not use for
Do not use this code for Dravet syndrome without intractability or without status epilepticus. Do not apply it to unspecified epilepsy, seizure disorder, or a past episode that is no longer active.
Coding tip
Verify that the chart explicitly links Dravet syndrome, intractability, and status epilepticus before assigning G40.833.