ICD-10 Code G40.83 – Dravet Syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.83 – Dravet syndrome
What it is
G40.83 identifies Dravet syndrome, a severe epilepsy syndrome that usually begins in infancy or early childhood. Use it for documented Dravet syndrome, not for nonspecific seizure disorders.
Clinical signs
Typical features include recurrent seizures that are often prolonged, difficult to control, and may be triggered by fever or illness. Developmental slowing, ataxia, or other neurologic impairment may be noted; clinical features vary, refer to documentation.
When to use this code
Use G40.83 when the provider documents Dravet syndrome by name or clearly confirms the diagnosis. It is appropriate on inpatient, outpatient, and problem-list records when the condition is active or being managed. If the note only says epilepsy or convulsions, check documentation for a more specific diagnosis.
Do not use for
Do not use this code for unspecified epilepsy, febrile seizures, or a single seizure event without a Dravet diagnosis. Check documentation if the record mentions another epilepsy syndrome or only a family history.
Coding tip
Code G40.83 only when the clinician explicitly links the seizure disorder to Dravet syndrome.