ICD-10 Code D82.1 – Di George’s syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D82.1 – Di George’s syndrome
What it is
D82.1 identifies Di George’s syndrome, a congenital condition caused by abnormal development involving the thymus and parathyroid glands. It is used when the diagnosis is documented as DiGeorge syndrome or a closely related named form.
Clinical signs
Clinical features vary; refer to documentation. Commonly reported findings include immune deficiency, hypocalcemia, congenital heart defects, and characteristic facial features. Some patients also have feeding, developmental, or speech problems.
When to use this code
Use D82.1 when the provider documents Di George’s syndrome as the confirmed diagnosis, including congenital immune or developmental abnormalities consistent with the syndrome. Apply it for encounters focused on evaluation, monitoring, or management of the condition. Check documentation if the record only mentions suspected features without a named syndrome.
Do not use for
Do not use this code for isolated hypocalcemia, heart defects, or immune deficiency without documentation of Di George’s syndrome. If the chart uses another specific syndrome name or uncertain wording, check documentation.
Coding tip
Code the syndrome only when the provider links the findings to Di George’s syndrome by name.