ICD-10 Code D58.9 – Hereditary Hemolytic Anemia, Unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D58.9 – Hereditary hemolytic anemia, unspecified
What it is
D58.9 identifies a hereditary hemolytic anemia when the specific inherited cause is not documented. It means red blood cells break down too early, but the chart does not name a more precise subtype.
Clinical signs
Clinical features vary; refer to documentation. Common findings in hereditary hemolysis include anemia, jaundice, splenomegaly, and a family history of similar disease or lifelong hemolytic episodes.
When to use this code
Use this code when the provider documents a hereditary hemolytic anemia but does not specify the type, such as hereditary spherocytosis or enzyme deficiency. It is also appropriate when records confirm an inherited hemolytic process without a more detailed diagnosis.
Check documentation if the note names a specific hereditary disorder, because a more precise code may apply. Code the unspecified form only when the available record truly lacks detail.
Do not use for
Do not use D58.9 for acquired hemolytic anemia, autoimmune hemolysis, or hemolytic anemia from nonhereditary causes. If the hereditary subtype is stated, code that specific condition instead.
Coding tip
Query the provider when the record says “hereditary hemolytic anemia” but does not identify the exact disorder.