ICD-10 Code C88.40 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C88.40 – Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission
What it is
This code identifies a documented extranodal marginal zone B-cell lymphoma of MALT type that has not achieved remission. Use it when the record states the lymphoma is active, persistent, or not in remission.
Clinical signs
Clinical features vary; refer to documentation. MALT lymphoma often presents as a localized extranodal mass or organ-specific symptoms, and diagnosis is usually confirmed by pathology and imaging.
When to use this code
Use C88.40 when the provider documents MALT lymphoma and states it has not achieved remission. This may apply at initial diagnosis, during ongoing disease, or when follow-up notes confirm persistent disease.
Code it only when the record clearly supports the nonremission status. If the site, laterality, or remission status is unclear, check documentation before assigning the code.
Do not use for
Do not use this code for MALT lymphoma in remission or when the chart does not specify remission status. Check documentation if the diagnosis is another lymphoma type or a nonspecific lymphoid malignancy.
Coding tip
Confirm both the MALT lymphoma diagnosis and the “not having achieved remission” wording in the provider note before coding.