ICD-10 Code C88.00 – Waldenström macroglobulinemia not having achieved remission (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C88.00 – Waldenström macroglobulinemia not having achieved remission
What it is
This code identifies Waldenström macroglobulinemia that is still active and has not reached remission. It is a lymphoplasmacytic lymphoma associated with an IgM-producing disorder.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include anemia, fatigue, enlarged lymph nodes or spleen, and symptoms related to hyperviscosity or neuropathy.
When to use this code
Use C88.00 when the record clearly states Waldenström macroglobulinemia and documents that remission has not been achieved. You should also use it when the provider describes persistent, active disease without remission status. Check documentation if the chart only notes a history of the condition.
Do not use for
Do not use this code if the record documents remission, since a different code applies. Do not assign it for nonspecific monoclonal gammopathy or other lymphomas unless Waldenström macroglobulinemia is specifically documented.
Coding tip
Verify the provider’s remission status wording before coding, because the “not having achieved remission” detail changes the code selection.