ICD-10 Code C46.9 – Kaposi’s sarcoma, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C46.9 – Kaposi’s sarcoma, unspecified
What it is
C46.9 identifies Kaposi’s sarcoma when the site or specific form is not documented. Use it for this vascular tumor diagnosis when the record confirms Kaposi’s sarcoma but gives no further detail.
Clinical signs
Clinical features vary; refer to documentation. Typical findings include violaceous skin lesions, plaques, or nodules, and the diagnosis may also involve mucosal or visceral disease.
When to use this code
Use C46.9 when the provider documents Kaposi’s sarcoma without naming a site, such as skin, soft tissue, or another organ. It is also appropriate when the note confirms the diagnosis but does not specify the anatomic location or subtype.
If later documentation identifies a more specific site, code that more detailed option instead. Check documentation for any associated HIV disease, transplant history, or other context, but do not infer those conditions from the Kaposi’s sarcoma diagnosis alone.
Do not use for
Do not use this code when the record names a specific Kaposi’s sarcoma site or when the diagnosis is only suspected. Do not use it for unrelated vascular lesions or other skin tumors.
Coding tip
Query for the primary site and any linked conditions when the note says only “Kaposi’s sarcoma.”