ICD-10 Code C46.3 – Kaposi’s sarcoma of lymph nodes (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C46.3 – Kaposi’s sarcoma of lymph nodes
What it is
C46.3 identifies Kaposi’s sarcoma involving lymph nodes. It is a malignant vascular tumor coded when documentation specifically states lymph node involvement.
Clinical signs
Clinical features vary; refer to documentation. Lymph node disease may be noted with enlarged nodes or biopsy-confirmed Kaposi’s sarcoma in nodal tissue.
When to use this code
Use C46.3 when the provider documents Kaposi’s sarcoma of lymph nodes, or when pathology confirms nodal involvement. Code it only when the record clearly identifies the lymph nodes as the site.
If the note describes Kaposi’s sarcoma elsewhere, choose the site-specific code that matches the documented location. Check documentation when the anatomic site is unclear or mixed.
Do not use for
Do not use this code for Kaposi’s sarcoma limited to skin, mucosa, or other organs. Do not assign it for nonspecific lymphadenopathy without documented Kaposi’s sarcoma.
Coding tip
Verify the exact anatomic site in the pathology or provider note before coding, because C46.3 is site-specific.