ICD-10 Code C46.0 – Kaposi’s sarcoma of skin (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C46.0 – Kaposi’s sarcoma of skin
What it is
C46.0 identifies Kaposi’s sarcoma involving the skin. It is a vascular neoplasm that most often appears as cutaneous lesions and may be part of a broader Kaposi’s sarcoma diagnosis.
Clinical signs
Typical findings include purple, red, or brown skin patches, plaques, or nodules. Clinical features vary; refer to documentation, especially if lesions are described as localized to skin only.
When to use this code
Use C46.0 when the provider documents Kaposi’s sarcoma of the skin, cutaneous Kaposi’s sarcoma, or skin-only involvement. It is appropriate when the record clearly supports a skin site without another specified site. Check documentation if the site is unclear or multi-site disease is described.
Do not use for
Do not use this code for Kaposi’s sarcoma documented in another site, such as lymph nodes or internal organs. If the note only says Kaposi’s sarcoma without a skin site, you need more specific documentation.
Coding tip
Code the documented anatomic site exactly; when skin involvement is stated, choose C46.0 rather than a nonspecific Kaposi’s sarcoma code.