ICD-10 Code G11.3 – Cerebellar ataxia with defective DNA repair (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G11.3 – Cerebellar ataxia with defective DNA repair
What it is
G11.3 identifies cerebellar ataxia linked to defective DNA repair. Use it for a hereditary neurologic disorder where impaired DNA repair is the underlying cause of cerebellar dysfunction.
Clinical signs
Typical findings include gait unsteadiness, limb incoordination, and other cerebellar signs. Clinical features vary; refer to documentation for the specific neurologic pattern and any associated genetic diagnosis.
When to use this code
Assign this code when the record clearly states cerebellar ataxia due to defective DNA repair or a named condition with that mechanism. Use it for confirmed diagnoses, not for nonspecific balance problems or suspected ataxia.
If the provider documents a broader inherited ataxia syndrome and specifies defective DNA repair, code the documented condition as directed. Check documentation when the cause is unclear or when the chart only says “ataxia.”
Do not use for
Do not use G11.3 for acquired ataxia, medication-related gait disturbance, or ataxia without documentation of defective DNA repair. Do not guess the etiology from testing alone.
Coding tip
Look for explicit provider linkage between the ataxia and defective DNA repair before assigning G11.3.