ICD-10 Code G11.5 – Hypomyelination – hypogonadotropic hypogonadism – hypodontia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G11.5 – Hypomyelination – hypogonadotropic hypogonadism – hypodontia
What it is
G11.5 identifies a rare inherited neurologic syndrome combining abnormal myelin formation, reduced gonadotropin-driven puberty, and missing teeth. Use it when the record clearly documents this specific triad.
Clinical signs
Typical findings include developmental or motor delay from hypomyelination, delayed or absent pubertal development from hypogonadotropic hypogonadism, and hypodontia. Clinical features vary; refer to documentation.
When to use this code
Use G11.5 when the provider diagnoses the full syndrome or explicitly links these findings to the named disorder. It may also apply when the chart documents the syndrome by its eponym or genetic diagnosis. Check documentation if only one component is mentioned.
Do not use for
Do not use this code for isolated hypodontia, isolated hypogonadotropic hypogonadism, or other leukodystrophies without the complete syndrome. Check documentation when the diagnosis is uncertain.
Coding tip
Code G11.5 only when the syndrome is stated; otherwise assign the separately documented conditions.