ICD-10 Code H49.812 – Kearns-Sayre syndrome, left eye (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H49.812 – Kearns-Sayre syndrome, left eye
What it is
Use this code for Kearns-Sayre syndrome affecting the left eye. It identifies a mitochondrial disorder with ocular involvement documented on the left side.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include external ophthalmoplegia, ptosis, and other eye movement abnormalities associated with Kearns-Sayre syndrome.
When to use this code
Assign H49.812 when the provider documents Kearns-Sayre syndrome limited to, or specifically involving, the left eye. Use it for confirmed diagnoses in ophthalmology, neurology, or genetics notes.
If the record only states Kearns-Sayre syndrome without laterality, check documentation before coding. Do not assume left eye involvement from general mitochondrial disease wording.
Do not use for
Do not use this code for unspecified laterality or for other eye disorders without documented Kearns-Sayre syndrome. Check documentation if the note does not clearly identify the left eye.
Coding tip
Verify laterality in the assessment or problem list before assigning H49.812.