ICD-10 Code G11.11 – Friedreich ataxia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G11.11 – Friedreich ataxia
What it is
G11.11 identifies Friedreich ataxia, an inherited neurodegenerative disorder that primarily affects coordination and movement. It is used when the diagnosis is documented and the condition is the reason for care.
Clinical signs
Typical findings include progressive gait and limb ataxia, dysarthria, and loss of deep tendon reflexes. Clinical features vary; refer to documentation for associated neurologic or cardiac findings.
When to use this code
Use G11.11 when the record clearly states Friedreich ataxia, including established or follow-up visits for the disorder. Code it when the provider documents this specific hereditary ataxia as the confirmed diagnosis. If the note only says “ataxia” without further detail, do not assume this code.
Do not use for
Do not use this code for nonspecific ataxia, cerebellar ataxia, or other hereditary ataxias unless Friedreich ataxia is documented. Check documentation if the diagnosis is uncertain or only suspected.
Coding tip
Verify the exact neurologic diagnosis in the assessment, because “ataxia” alone is not enough for G11.11.