ICD-10 Code E74.00 – Glycogen Storage Disease, Unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E74.00 – Glycogen storage disease, unspecified
What it is
E74.00 identifies glycogen storage disease when the specific type is not documented. It refers to an inherited disorder of glycogen metabolism, but you should not assume a subtype without clear provider documentation.
Clinical signs
Clinical features vary; refer to documentation. Commonly described findings in glycogen storage disorders include abnormal liver enlargement, low blood sugar episodes, muscle weakness, or exercise intolerance, depending on the type.
When to use this code
Use this code when the record states glycogen storage disease without naming a more specific subtype. It may also fit when the clinician documents a suspected or historical glycogen storage disorder and no further detail is available. Verify whether the chart supports a more specific code before assigning E74.00.
Do not use for
Do not use this code if the provider identifies a specific glycogen storage disease type. Do not code it for unrelated carbohydrate metabolism disorders or for a family history entry alone.
Coding tip
Review the assessment and problem list carefully; if the subtype is named anywhere in the record, code the more specific diagnosis instead.