ICD-10 Code L11 – Other acantholytic disorders (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L11 – Other acantholytic disorders
What it is
L11 identifies a group of uncommon skin disorders marked by acantholysis, meaning loss of cohesion between skin cells. Use it when documentation names an acantholytic disorder that is not classified elsewhere.
Clinical signs
Clinical features vary; refer to documentation. Standard descriptions may include fragile blisters, erosions, or crusted lesions, but the exact pattern depends on the specific disorder named by the clinician.
When to use this code
Use L11 when the provider documents an unspecified or other acantholytic disorder and no more specific ICD-10-CM code applies. It is appropriate when the record supports an acantholytic skin condition but does not identify a more precise diagnosis. Check documentation if the note is incomplete.
Do not use for
Do not use L11 when a more specific diagnosis is documented, such as a named blistering or pemphigus-related condition. Also avoid it if the record only describes a rash without evidence of acantholysis.
Coding tip
Code L11 only after confirming the provider’s wording includes “acantholytic” or an equivalent diagnosis.