ICD-10 Code E74.03 – Cori disease (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E74.03 – Cori disease
What it is
Cori disease is an inherited glycogen storage disorder caused by a deficiency affecting glycogen breakdown. It leads to abnormal glycogen accumulation in the liver, muscles, or both.
Clinical signs
Clinical features vary; refer to documentation. Common findings include enlarged liver, low muscle tone, weakness, and growth delay, especially in childhood.
When to use this code
Use E74.03 when the provider documents Cori disease, Forbes disease, or glycogen storage disease type III. Code it for confirmed diagnoses in outpatient, inpatient, or problem-list documentation. If the record only says “glycogen storage disease” without type, check documentation.
Do not use for
Do not use this code for other glycogen storage disorders or for suspected disease without confirmation. Avoid it when the chart documents a different metabolic disorder.
Coding tip
Verify the exact glycogen storage disease type in the note before assigning E74.03.