ICD-10 Code E72.530 – Primary hyperoxaluria, type 1 (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E72.530 – Primary hyperoxaluria, type 1
What it is
E72.530 identifies primary hyperoxaluria type 1, a rare inherited disorder that causes excessive oxalate production. The excess oxalate can accumulate in the kidneys and other tissues.
Clinical signs
Common findings include recurrent kidney stones, nephrocalcinosis, hematuria, and progressive kidney dysfunction. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents primary hyperoxaluria type 1 or confirms the diagnosis in the chart. It also applies when the condition is being managed as a known inherited oxalate disorder, even if current symptoms are not detailed. Check documentation if the type is not specified.
Do not use for
Do not use this code for secondary hyperoxaluria, nonspecific hyperoxaluria, or kidney stones without documentation of primary hyperoxaluria type 1. Check documentation.
Coding tip
Capture the exact type documented, because E72.530 is specific to primary hyperoxaluria type 1.