ICD-10 Code E72.03 – Lowe’s syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E72.03 – Lowe’s syndrome
What it is
E72.03 identifies Lowe syndrome, a rare inherited disorder that affects the eyes, brain, and kidneys. It is used when the diagnosis is documented as Lowe syndrome or oculocerebrorenal syndrome.
Clinical signs
Typical findings include congenital cataracts, developmental delay or intellectual disability, and kidney tubular dysfunction. Clinical features vary; refer to documentation.
When to use this code
Use E72.03 when the provider documents Lowe syndrome as the confirmed diagnosis. It may also apply when the record describes the classic oculocerebrorenal pattern and the clinician links it to this syndrome. Do not code from suspicion alone; check documentation.
Do not use for
Do not use this code for isolated cataracts, nonspecific developmental delay, or kidney disease without a documented diagnosis of Lowe syndrome. If the record is unclear, check documentation.
Coding tip
Confirm the exact syndrome name in the assessment or problem list before assigning E72.03.