ICD-10 Code J84.82 – Adult pulmonary Langerhans cell histiocytosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code J84.82 – Adult pulmonary Langerhans cell histiocytosis
What it is
J84.82 identifies adult pulmonary Langerhans cell histiocytosis, a rare lung disorder involving abnormal Langerhans cell infiltration. It is coded when the condition is documented as affecting the lungs in an adult.
Clinical signs
Clinical features vary; refer to documentation. Commonly described findings include cough, shortness of breath, and imaging evidence of cystic or nodular lung disease, often in adults with a compatible clinical picture.
When to use this code
Use J84.82 when the provider documents adult pulmonary Langerhans cell histiocytosis, pulmonary Langerhans cell histiocytosis in an adult, or an equivalent diagnosis. You should also use it when the record clearly localizes the disease to the lungs. Check documentation if the note is ambiguous or uses a broader histiocytosis term.
Do not use for
Do not use this code for pediatric Langerhans cell histiocytosis or for histiocytosis not specified as pulmonary. If the diagnosis is uncertain, check documentation before coding.
Coding tip
Code the condition only when the record explicitly supports adult pulmonary involvement; otherwise, query for clarification.