ICD-10 Code H57.01 – Argyll Robertson pupil, atypical (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H57.01 – Argyll Robertson pupil, atypical
What it is
This code identifies an atypical Argyll Robertson pupil, a pupil abnormality documented on eye examination. You use it when the record specifically describes this finding rather than a broader neurologic or infectious diagnosis.
Clinical signs
Clinical features vary; refer to documentation. Standard descriptions include pupils that respond poorly to light but better to near focus, with an irregular or small appearance. Confirm the abnormality is documented by the clinician.
When to use this code
Use this code when the provider documents atypical Argyll Robertson pupil as the diagnosis or exam finding. It may appear in ophthalmology, neurology, or general exam notes. Code it only when the chart supports that specific pupil abnormality.
Do not use for
Do not use it for general anisocoria, fixed pupil, or unspecified pupillary abnormality. If the note does not clearly identify atypical Argyll Robertson pupil, check documentation before assigning H57.01.
Coding tip
Code the exact documented pupil abnormality and avoid substituting a broader eye symptom code.