ICD-10 Code H55.01 – Congenital nystagmus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H55.01 – Congenital nystagmus
What it is
Congenital nystagmus is a lifelong involuntary eye movement disorder present from birth or early infancy. Use this code when documentation identifies nystagmus as congenital rather than acquired.
Clinical signs
Typical findings include rhythmic, uncontrolled eye movements and reduced visual stability. Clinical features vary; refer to documentation for onset, laterality, and any associated ocular findings.
When to use this code
Use H55.01 when the record clearly states congenital nystagmus, infantile nystagmus, or nystagmus present since birth. It is appropriate when the provider documents the condition as a primary diagnosis or as a confirmed finding. If the record only says “nystagmus” without onset, check documentation.
Do not use for
Do not use this code for acquired nystagmus or for transient eye movements caused by drugs, neurologic disease, or acute illness. If the type is unspecified, check documentation before coding.
Coding tip
Verify that the chart supports congenital onset; the distinction from acquired nystagmus drives correct code selection.