ICD-10 Code G40.C11 – Lafora Progressive Myoclonus Epilepsy, Intractable, with Status Epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.C11 – Lafora progressive myoclonus epilepsy, intractable, with status epilepticus
What it is
This code identifies Lafora progressive myoclonus epilepsy that is not controlled by treatment and has occurred with status epilepticus. Use it for the specific inherited epilepsy syndrome, not for general seizure disorders.
Clinical signs
Typical findings include progressive myoclonus, generalized seizures, and neurologic decline over time. Status epilepticus must be documented; clinical features vary, so refer to documentation.
When to use this code
Use this code when the record clearly states Lafora progressive myoclonus epilepsy and describes it as intractable. The chart should also document status epilepticus, current or past, tied to this diagnosis.
Assign it from neurology notes, discharge summaries, or problem lists when the diagnosis is explicit. If the note only says epilepsy, myoclonus, or seizure disorder, check documentation before coding.
Do not use for
Do not use for unspecified epilepsy, isolated myoclonus, or seizures without the Lafora diagnosis. Do not use if status epilepticus or intractability is not documented.
Coding tip
Match all three elements in the note: Lafora epilepsy, intractable, and status epilepticus.