ICD-10 Code G40.B01 – Juvenile myoclonic epilepsy, not intractable, with status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.B01 – Juvenile myoclonic epilepsy, not intractable, with status epilepticus
What it is
Use this code for juvenile myoclonic epilepsy (JME) when the seizure disorder is not intractable and the patient has had status epilepticus. JME is an epilepsy syndrome that typically includes myoclonic seizures and may also include generalized tonic-clonic seizures.
Clinical signs
Typical features include brief, sudden muscle jerks, often soon after waking, and generalized seizure activity. Clinical features vary; refer to documentation, especially for confirmation of status epilepticus and the JME diagnosis.
When to use this code
Use this code when the record clearly identifies juvenile myoclonic epilepsy, states it is not intractable, and documents status epilepticus. You may also use it when the provider links a current seizure episode to established JME in the assessment or problem list.
Do not use for
Do not use this code if the epilepsy is documented as intractable, if status epilepticus is not present, or if the seizure type is unspecified. Check documentation when the record does not clearly identify juvenile myoclonic epilepsy.
Coding tip
Verify both the epilepsy subtype and the status epilepticus qualifier before assigning G40.B01.