ICD-10 Code E84 – Cystic fibrosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E84 – Cystic fibrosis
What it is
Cystic fibrosis is an inherited disorder that affects the lungs, pancreas, and other organs. It causes thick, sticky secretions that can block airways and ducts.
Clinical signs
Common findings include chronic cough, recurrent respiratory infections, wheezing, poor weight gain, and digestive problems. Clinical features vary; refer to documentation.
When to use this code
Use E84 when the provider documents cystic fibrosis, including confirmed diagnosis or established history of the condition. It may also apply when the record clearly identifies cystic fibrosis as the reason for ongoing management or evaluation.
Check the note for any specified manifestations or organ involvement that require additional coding. Do not assume complications without provider documentation.
Do not use for
Do not use E84 for unrelated chronic lung disease, asthma, or isolated pancreatic problems without cystic fibrosis. Check documentation if the diagnosis is only suspected or ruled out.
Coding tip
Code cystic fibrosis only when the diagnosis is explicitly documented, and add manifestation codes only if the record supports them.