ICD-10 Code E84.1 – Cystic fibrosis with intestinal manifestations (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E84.1 – Cystic fibrosis with intestinal manifestations
What it is
This code identifies cystic fibrosis when the intestinal tract is affected. Use it for documented intestinal involvement as part of CF, not for cystic fibrosis without bowel manifestations.
Clinical signs
Clinical features vary; refer to documentation. Intestinal involvement may include meconium ileus, distal intestinal obstruction, or other bowel complications linked to cystic fibrosis.
When to use this code
Use E84.1 when the provider documents cystic fibrosis with intestinal manifestations in the assessment or problem list. It is appropriate when the record links the intestinal condition to CF, such as bowel obstruction related to the disease.
Do not use for
Do not use this code for cystic fibrosis without intestinal involvement, or when the bowel problem is documented as unrelated. Check documentation if the record does not clearly connect the intestinal findings to CF.
Coding tip
Confirm the intestinal manifestation is explicitly documented as part of cystic fibrosis before assigning E84.1.