ICD-10 Code E80.29 – Other porphyria (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E80.29 – Other porphyria
What it is
E80.29 identifies porphyria types that do not have a more specific ICD-10-CM code. Use it for documented porphyrin metabolism disorders when the record does not name a narrower subtype.
Clinical signs
Clinical features vary; refer to documentation. Porphyrias may present with recurrent abdominal pain, photosensitivity, neuropathic symptoms, or dark urine, depending on the specific disorder.
When to use this code
Use this code when the provider documents “other porphyria,” a porphyria not otherwise classified, or an unspecified porphyrin metabolism disorder that cannot be assigned to a more specific code. It is appropriate when the chart supports porphyria but does not identify the exact type. Check documentation if the subtype is unclear.
Do not use for
Do not use E80.29 when the record identifies a specific porphyria with its own code, or when the diagnosis is only suspected. If the condition is not confirmed, code the documented symptoms instead.
Coding tip
Review the provider’s exact porphyria terminology first, because a more specific ICD-10-CM code may apply.