ICD-10 Code E80.1 – Porphyria cutanea tarda (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E80.1 – Porphyria cutanea tarda
What it is
E80.1 identifies porphyria cutanea tarda, a disorder of heme metabolism that causes photosensitive skin disease. It is used when the diagnosis is documented and you need the specific ICD-10-CM code.
Clinical signs
Typical findings include fragile skin, blistering, and increased skin sensitivity on sun-exposed areas, especially the hands and forearms. Clinical features vary; refer to documentation.
When to use this code
Use E80.1 when the provider documents porphyria cutanea tarda as the confirmed diagnosis. It is appropriate for encounters focused on evaluation, follow-up, or management of this condition. Code it when the record clearly identifies the disorder, even if symptoms are not fully detailed.
Do not use for
Do not use this code for unspecified porphyria or for other porphyria types unless the record specifically states porphyria cutanea tarda. Check documentation if the diagnosis is uncertain or only suspected.
Coding tip
Assign the most specific porphyria code documented; if the note only says “porphyria,” do not assume E80.1.